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Trigonocephaly

**Trigonocephaly**
*Classification & external resources*
ICD-10	Q75.0
ICD-9	756.0
DiseasesDB	33252

Trigonocephaly is a type of cephalic disorder. This is the premature fusion of the metopic suture (part of the frontal suture which joins the two halves of the frontal bone of the skull) in which a V-shaped abnormality occurs at the front of the skull. It is characterized by the triangular prominence of the forehead and closely set eyes. Genetic testing may be offered to determine the cause and recurrence risk.

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Treatment

Surgery can greatly reduce the visual effects of trigonocephaly. It can also help address comorbid elevated intracranial pressure.^[1]

History

It is believed that the first surgery to correct the disorder was successfully completed in early 1962 in San Diego, California, on a six-month-old girl.^[2]

References

^ Shimoji T, Tomiyama N (2004). "Mild trigonocephaly and intracranial pressure: report of 56 patients". Childs Nerv Syst 20 (10): 749–56. doi:10.1007/s00381-004-0970-y. PMID 15185114.
^ Anerson FM, Gwinn JL, Todt JC (1962). "Trigonocephaly. Identity and surgical treatment". J. Neurosurg. 19: 723–30. PMID 13861226.

v • d • e Congenital malformations and deformations of musculoskeletal system (Q65-Q79, 754-756)
Limbs	hip: Dislocation of hip/Hip dysplasia feet (Club foot, Flat feet, Pes cavus) head, face, spine and chest: skull, face and jaw (Dolichocephaly, Plagiocephaly) - Scoliosis - chest (Pectus excavatum, Pectus carinatum) Polydactyly/Syndactyly (Webbed toes) reduction deficits (Ectrodactyly, Amelia, Phocomelia) upper limb (Cleidocranial dysostosis, Madelung's deformity, Sprengel's deformity) knee (Genu valgum, Genu varum) Arthrogryposis
Skull and face bones	Craniosynostosis (Scaphocephaly) - Trigonocephaly - Oxycephaly - Crouzon syndrome - Hypertelorism - Macrocephaly - Treacher Collins syndrome - Platybasia
Spine and bony thorax	Klippel-Feil syndrome - Spondylolisthesis - Cervical rib - Bifid rib
Osteochondrodysplasia	growth of tubular bones and spine: Achondrogenesis - Thanatophoric dysplasia - Short rib-polydactyly syndrome - Chondrodysplasia punctata (Rhizomelic chondrodysplasia punctata, Conradi-Hünermann syndrome), Achondroplasia (Hypochondroplasia, Osteosclerosis congenita) - Ellis-van Creveld syndrome - Spondyloepiphyseal dysplasia congenita Osteogenesis imperfecta - McCune-Albright syndrome - Osteopetrosis - Metaphyseal dysplasia - Hereditary multiple exostoses - Osteopoikilosis - Chondrodystrophy - Osteodystrophy
Other	abdominal wall (Congenital diaphragmatic hernia, Omphalocele, Gastroschisis, Prune belly syndrome) - Ehlers-Danlos syndrome
See also non-congenital conditions (M, 710-739)

Categories: Skeletal disorders | Congenital disorders

This article is licensed under the GNU Free Documentation License. It uses material from the Wikipedia article "Trigonocephaly". A list of authors is available in Wikipedia.